Get Web page suited for printing
Email this to a friend or colleague


Table of Contents (click to jump to sections)

What is Hydrocephalus?
Is there any treatment?
What is the prognosis?
What research is being done?

Organizations
Related NINDS Publications

What is Hydrocephalus?
Hydrocephalus is a condition in which the primary characteristic is excessive accumulation of fluid in the brain. Although hydrocephalus was once known as "water on the brain," the "water" is actually cerebrospinal fluid (CSF) -- a clear fluid surrounding the brain and spinal cord. The excessive accumulation of CSF results in an abnormal dilation of the spaces in the brain called ventricles. This dilation causes potentially harmful pressure on the tissues of the brain. Hydrocephalus may be congenital or acquired. Congenital hydrocephalus is present at birth and may be caused by either environmental influences or genetic predisposition. Acquired hydrocephalus develops at the time of birth or at some point afterward. Acquired hydrocephalus can affect individuals of all ages and may be caused by injury or disease. The causes of hydrocephalus are not all well understood. Symptoms of hydrocephalus vary with age, disease progression, and individual differences in tolerance to CSF. In infancy, the most obvious indication of hydrocephalus is often the rapid increase in head circumstance or an unusually large head size. In older children and adults, symptoms may include headache followed by vomiting, nausea, papilledema (swelling of the optic disk, which is part of the optic nerve), downward deviation of the eyes (called "sunsetting"), problems with balance, poor coordination, gait disturbance, urinary incontinence, slowing or loss of development, lethargy, drowsiness, irritability, or other changes in personality or cognition, including memory loss. Hydrocephalus is diagnosed through clinical neurological evaluation and by using cranial imaging techniques such as ultrasonography, computer tomography (CT), magnetic resonance imaging (MRI), or pressure-monitoring techniques.

Is there any treatment?
Hydrocephalus is most often treated with the surgical placement of a shunt system. This system diverts the flow of CSF from a site within the central nervous system to another area of the body where it can be absorbed as part of the circulatory process. A shunt is a flexible but study silastic tube. A limited number of patients can be treated with an alternative procedure called third ventriculostomy. In this procedure, a small hole is made in the floor of the third ventricle, allowing the CSF to bypass the obstruction and flow toward the site of resorption around the surface of the brain.

What is the prognosis?
The prognosis for patients diagnosed with hydrocephalus is difficult to predict, although there is some correlation between the specific cause of hydrocephalus and the patient's outcome. Prognosis is further complicated by the presence of associated disorders, the timeliness of diagnosis, and the success of treatment. Affected individuals and their families should be aware that hydrocephalus poses risks to both cognitive and physical development. Treatment by an interdisciplinary team of medical professionals, rehabilitation specialists, and educational experts is critical to a positive outcome. Many children diagnosed with the disorder benefit from rehabilitation therapies and educational interventions, and go on to lead normal lives with few limitations.

What research is being done?
The NINDS conducts and supports a wide range of fundamental studies that explore the complex mechanisms of normal brain development. The knowledge gained from these studies provides the foundation for understanding how this process can go awry and, thus, offers hope for new means to treat and prevent developmental brain disorders such as hydrocephalus.

2618 Avenue Z
Brooklyn NY 11235-2023
GHRF2618@aol.com

Tel: 718-743-GHRF (-4473) 800-458-8655
Fax: 718-743-1171

Hydrocephalus Association

870 Market Street
Suite 705
San Francisco CA 94102
hydroassoc@aol.com
www.hydroassoc.org
Tel: 415-732-7040 888-598-3789
Fax: 415-732-7044

Hydrocephalus Support Group, Inc.

P.O. Box 4236
Chesterfield MO 63006-4236
dhydrobuff@aol.com
Tel: 636-532-8228