Re: CREST syndrome

Posted By CCF CARDIO MD - CRC on September 09, 1998 at 11:22:18:

In Reply to: CREST syndrome posted by Beth on September 07, 1998 at 18:18:01:






My mother was diagnosed with CREST syndrome ~10 months ago.  She has developed pulmonary hypertension as a result of this. Most information I was able to read about CREST talked about its slow progress and generally more benign outcome(than full blown scleroderma). Is this still the case since she has developed pulmonary hypertension?  Lasix has not helped and she really is fatigued.  She would like to know if she can hope to feel better.  She is being referrred to Cleveland for possible treatment with prostacyclin.  Any info you can provide would be most appreciated.
Thank you.
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Dear Beth,
Thank you for your question.  This is really more of a question for a pulmonary specialist since they have more expertise in this area.   In general, pulmonary hypertension can range from mild to severe.  Severe pulmonary hypertension may require lung transplantation.  Prostacycline is a iv medication that helps to lower the pressures in the lung.  Hope this little bit of information helps.  

Information provided here is for educational purposes only.  It is not intended to replace your doctor's advice.  Only your doctor can make specific diagnoses and recommend treatment.  If you would like to be seen at the Cleveland Clinic please call 1-800-CCF-CARE and ask for an appointment with a cardiologist.