CCTGA

[carol77]

Hello, I have a 4 year old that has cctga. She is doing perfect! No meds. Her doctor told us everything seems to be balanced. She has not had any surgeries.  He also said her pressures are balanced.  He thinks we should not press for surgery until we are forced. I would just like a second opinion. She does have a little tricuspid leakage, pul. stenosis, and a large vsd.  We just pray that she continues to do so well. Is this normal for children with a heart problem like this to go so long without surgery and is it a good idea to just leave things alone.  Thanks.

[bobqin]

A related discussion, cctga. 7 year old was started.

[shivic007]

hi we had our first baby very normal and healthy and now once again my wife is 23 weeks pregnant today the doctor had detected that our unborn child has a cctga and vsd problem . we are very much shattered with this news and dont know what to do should we carry out our pregnancy or end it please advise us as we cant see our child dieing after he is born . please we need ur expert opinion . can you tell us what are the consequences of this defect

[Marie M Gleason, M.D.]

As you know congenitally corrected transposition of the great arteries (CCTGA) is a very complex problem.  There are no hard and fast rules about surgical intervention.  The major concern is the ability of the anatomic right ventricle (RV) to continue to do the workload of the body that is normally handled by the left ventricle (LV) over many years.  It sounds like your daughter does have a complicated case if she has L-TGA with a large VSD and pulmonary stenosis.  Your cardiologist must be sure that the pulmonary artery pressure is normal if the VSD is large.  They also must be following the function of the RV.  We cannot comment on type or timing of intervention in a forum like this.  It is always decided on a case-by-case basis.  Since a double-switch operation is a complicated and risky operation, much thought needs to go into it before a patient is referred for surgery.