hi my name is fatema from india.my son is 17.He has had severe ebsteins anomaly of the tricuspid valve and he has had a bi directional glenn shunt operation five years before . he is doing fine except that he is looking a little more blue. Is fontan required now or we can wait.
Ebstein’s anomaly of the tricuspid valve is downward displacement of the septal leaflet of the tricuspid valve, with varying degrees of abnormality of the other two leaflets of the valve. In your son’s case, his valve was so abnormal and was significantly obstructing outflow to the lungs that he required a bidirectional Glenn shunt to allow blood to get to the lungs. For our other readers, this is where the superior vena cava, the vein that drains the head and neck veins, is attached directly into the pulmonary arteries, bypassing the right side of the heart and allowing that blood to get to the lungs.
Without evaluating your son further, I cannot say if a Fontan is warranted or, at this late stage, whether he would even survive it. He most likely would need a cardiac catheterization to evaluate his anatomy and hemodynamics to see if his heart function is adequate and the blood pressure across his lungs are low enough. This would give more information to say whether this would be required. There are some centers that are able to repair the tricuspid valve and to make it functional; I cannot say if your son’s tricuspid valve would be a candidate for this, though.
Thankyou so much for your reply. Your comment about he surviving the fontan at this age has got me worried. If his glenn shunt is performing well then is not advisable to wait? Is there an age limit for a fontan surgery to be performed? Im getting his 2decho done today to get a clear picture.
Will get back to you with the reports.
Copyright 1994-2017MedHelp International.All rights reserved. MedHelp is a division of Aptus Health.
The Content on this Site is presented in a summary fashion, and is intended to be used for educational and entertainment purposes only. It is not intended to be and should not be interpreted as medical advice or a diagnosis of any health or fitness problem, condition or disease; or a recommendation for a specific test, doctor, care provider, procedure, treatment plan, product, or course of action. Med Help International, Inc. is not a medical or healthcare provider and your use of this Site does not create a doctor / patient relationship. We disclaim all responsibility for the professional qualifications and licensing of, and services provided by, any physician or other health providers posting on or otherwise referred to on this Site and/or any Third Party Site. Never disregard the medical advice of your physician or health professional, or delay in seeking such advice, because of something you read on this Site. We offer this Site AS IS and without any warranties. By using this Site you agree to the following Terms and Conditions. If you think you may have a medical emergency, call your physician or 911 immediately.