Cystic fibrosis (CF) is a genetic disease of the exocrine glands affecting the gastrointestinal and respiratory systems. Sweat electrolytes, like sodium and chloride, are high at birth. Thick mucus can block the small airways. The problem usually becomes evident and is diagnosed in infancy or childhood. Occasionally it is diagnosed later, in the 3rd and 4th decades of life. It occurs with a wide range of severity. The minority of people with very mild forms of the disease may live into their 50's and 60's. To live into their 70's is extraordinary but not impossible. While it is possible that your uncle has CF, it is most unlikely that it wouldn’t have been evident prior to the age of 73.
The diagnosis of CF can be made by what is called a "Sweat test" and also by genetic testing. Your uncle’s doctor should be asked about the basis for the diagnosis of CF at his age.
The pulmonary condition called bronchiectasis can occur with CF but also can occur without CF. Bronchiectasis is a problem where mucus collects in the airways of the lungs. It can be difficult to clear the mucus because of damage to the normal methods that the lungs use to clear mucus. This can lead to episodes of infection. Your uncle may have bronchiectasis and the assumption has been made that it is due to CF.
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