Cystic renal dysplasia, defined by microscopic features, is an anomaly of differentiation of the fetal kidney. As a result, the kidney contains primitive ducts and nonrenal tissues such as cartilage, fat, hematopoietic tissue, and often cysts.
This condition has a sporadic inheritance pattern and may be part of a larger disease. It can be differentiated from polycystic kidney disease via imaging studies.
Other cystic kidney diseases can include the following:
* Autosomal recessive and, less commonly, autosomal dominant polycystic kidney disease.
* Familial juvenile nephronophthisis and medullary cystic kidney disease.
* Medullary sponge kidney.
* von Hippel-Lindau disease and tuberous sclerosis.
As mentioned above, renal dysplasia has a variable genetic pattery and may be part of a larger disease. Once that larger disease is diagnosed, then the inheritance pattern can be clearer.
Followup with your personal physician is essential.
This answer is not intended as and does not substitute for medical advice - the information presented is for patient education only. Please see your personal physician for further evaluation of your individual case.
Thanks,
Kevin, M.D.
Bibliography:
Niaudet. Renal cystic diseases in children. UptoDate, 2004.
