Alpha 1-proteinase inhibitor is a protein, also called alpha 1-antitrypsin. This protein
occurs naturally in the body and is important for preventing the breakdown of tissues in the
lungs.
In people who lack the alpha 1-antitrypsin protein, breakdown of lung tissues can lead to
emphysema (damage to the air sacs in the lungs).
Alpha 1-proteinase inhibitor is used to treat alpha 1-antitrypsin deficiency in people who
have symptoms of emphysema.
Alpha 1-antitrypsin deficiency is a genetic (inherited) disorder and alpha 1-proteinase
inhibitor will not cure this condition.
Alpha 1-proteinase inhibitor may also be used for other purposes not listed in this
medication guide.